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Table 3 DHS clinical manifestations.

From: The Dapsone Hypersensitivity Syndrome revisited: a potentially fatal multisystem disorder with prominent hepatopulmonary manifestations

Systemic

   1. Fever*

   2. Pneumonitis*

   3. Lymphadenopathy

   4. Hepatitis*

   5. Hemolytic anemia*

   6. Carditis

Dermatological

   1. Exfoliative dermatitis

   2. Eczematous/maculopapular eruption*

   3. Oral erosions

   4. Vesicles and bullae

   5. Photosensitivity

Laboratory

   1. Hemolysis*

   2. Anemia*

   3. Eosinophilia

   4. Atypical lymphocytosis

   5. Transaminitis/elevated bilirubin/alkaline phosphatase*

   6. Hypogammaglobulinemia

  1. *-manifestations present in the patient described.